IgG4-related systemic sclerosing disease: a diagnosis to be considered

IgG4-related sclerosing disease.

Based on histological and immunohistochemical examination of various organs of patients with autoimmune pancreatitis (AIP), a novel clinicopathological entity of IgG4-related sclerosing disease has been proposed. This is a systemic disease that is characterized by extensive IgG4-positive plasma cells and T-lymphocyte infiltration of various organs. Clinical manifestations are apparent in the pa...

Kidney involvement by IgG4-related sclerosing disease

A 54-year-old Caucasian woman was admitted due to persistent febrile syndrome, sweating and abdominal pain. Fever marked the onset of the patient’s medical history 10 years earlier. The physical examination revealed normal findings. Laboratory data showed normal white blood cell count, mild microcytic anaemia with a normal reticulocyte count, important inflammatory syndrome (C-reactive protein ...

IgG4-related sclerosing cholangitis.

IgG4-Related Sclerosing Mesenteritis

© 2016 The Korean Society of Pathologists/The Korean Society for Cytopathology This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/ by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. pISSN 2383-7...

Usefulness of PET/CT imaging in systemic IgG4-related sclerosing disease. A report of three cases.

Autoimmune pancreatitis is the pancreatic manifestation of a novel clinicopathological disorder called systemic IgG4-related sclerosing disease. Beside the pancreas, this entity affects other sites (salivary glands, orbit, lung, thyroid, gallbladder, biliary tree system, kidney, abdominal aorta, retroperitoneum, prostate, and lymph node) by infiltration with IgG4-positive plasma cells. Several ...